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Buschke-Ollendorff syndrome

*Gene map locus 12q14
BOS
Dermatofibrosis lenticularis disseminata with osteopoikilosis
Dermatofibrosis, disseminated, with osteopoikilosis
Dermatoosteopoikilosis
Osteopathia condensans disseminata
Osteopoikilosis, isolated
[Clinical features: cutaneous lesions (disseminated lenticular dermatofibrosis); skeletal changes (osteopoikilosis)]
[Inheritance: autosomal dominant]

Buschke-Ollendorf Syndrome
Buschke-Ollendorf Syndrome
Buschke-Ollendorf Syndrome
DermIS
DermIS
DermIS

Dermatofibrosis Lenticularis (Buschke-Ollendorf Syndrome)
Dermatofibrosis Lenticularis (Buschke-Ollendorf Syndrome)
Dermatofibrosis Lenticularis (Buschke-Ollendorf Syndrome)
eMedicine
eMedicine
eMedicine

Dermatofibrosis Lenticularis (Buschke-Ollendorf Syndrome)
Dermatofibrosis Lenticularis (Buschke-Ollendorf Syndrome)
Dermatofibrosis Lenticularis (Buschke-Ollendorf Syndrome)
eMedicine
eMedicine
eMedicine

   
Buschke-Ollendorff syndrome, in which elastomas are associated with bony changes known as osteopoikilosis
   
MerckMedicus
   


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Edited by Aldo Campana, March 14, 2010